180                                                                                                                       Malignant Melanoma

33.         Malignant Melanoma

33.1                                General considerations

 

Stage of primary cutaneous melanoma

AJCC        T           N          M      Clinicopathological  details

Stage IA        T1           N0          M0             <0.75 mm Breslow thickness

Stage IB        T2            N0          M0             0.76-1.5mm

Stage IIA       T3           N0          M0             1.51-4.0mm

Stage IIB       T4            N0           M0            >4.0mm

Stage III        Any T      N1            M0           Nodal disease

Stage IV        Any T      any N      M1/2         Metastatic disease

 

                        Clark’s system (based on a qualitative description of the increasing levels

                         of penetration  through the dermis to the subcutaneous  fat)

                       

Level  I          Tumor remains above the intact basal lamina; melanoma in situ  (0mm)

Level  II         Tumor invades into the papillary dermis(≤ 0.75mm)

Level  III        Tumor reaches the papillary-reticular derims interface(0.76-1.5mm)

Level  IV       Tumor invades into the reticular dermis(1.6-3.9mm)

Level  V        Tumor invades into the subcutaneous fat(≥4mm)

 

                        Breslow’s system

Quantifies the vertical depth of invasion (in mm) from the granular layer of the epidermis(or the base of an ulcer) to the deepest identifiable contiguous melanoma cell.

                       

                        Therapeutic excision is the accepted primary  treatment for localized disease. If surgery is not possible, radiotherapy with curative intention can also be applied. Regional lymph node dissection must  be conducted in case of  regional lymph node metastases.

 

                        Isolated regional parfusion is indicated for inoperable tumor confined to an extremity.

 

                        High-risk patients(primaries ≥4 mm deep, regional  lymph node involvement) often require adjuvant therapy in addition to surgery (interferon, radiotherapy, systemic therapy is still experimental).

 

                        Systemic therapy  for metastatic melanoma includes chemotherapy and biological therapy. In some studies combined immuno-chemotherapy (biochemotherapy) has shown high objective response rates and a small proportion of  longterm CRs, but also a substantial increase in toxicity.

 

                        Therapeutic vaccines have also started to show some evidence of clinical  effectiveness.

                       

                        Literature: for review e.g.

                                    BECKER et al, Clin.Exp.Dermatol.25 (2000):503-508(classical   

                                    chemotherapy)

                                    BONACCORSI et al,Dermatol.Clin. 19(2001): 727-735 (high-risk 

                                    melanoma)

                                    CHOWDHURY et al,Cancer Treat.Rev.25(1999):259-270(new

                                    approaches to systemic treatment).

 

Malignant Melanoma                                                                                                                              181

 

                                    DURAN GARCIA et al,Ann.Pharmacother.33(1999):730-738

                                    EGGERMONT, Recent Results Cancer Res.157(2000): 178-

                                    189(adjuvant therapy)

                                    KROON et al, Melanoma Res. 9(1999):207-212 (consensus of the 

                                    Dutch Melanoma Working Party)

                                    MA and ARIYAN,Clin.Plast.Surg.27(2000):441-450 (isolated 

                                    limb perfusion)

                                    MARCHAND et al, Expert Opin. Biol. Ther.1(2001):497-

                                    510(melanoma vaccines)

                                    MARGOLIN, Curr.Oncol.Rep.3 (2001):338-343(high-dose 

                                    therapy)

                                    PHILIP and FLAHERTY, Curr.Oncol.Rep.2(2000):314-

                                    321(biochemotherapy)

                                    WHITTAKER, Clin.Exp.Dermatol.25(2000):497-502(adjuvant 

                                     therapy)

 

33.2                                Single agent therapy: chemotherapy

 

33.2.1                         Dacarbazine (DTIC)

Dacarbazine           850-1000mg/m²               i.v.(short inf)                d1 or

                               250mg/m²                         i.v.(short inf)                d1-5

To be  repeated every 3-4 weeks

 

                        Literature:

                                    CHAPMAN et al,J.Clin.Oncol. 17(1999):2745-2751 (randomized   

                                    phase III study of  dacarbazine 1000mg/m² vs the Dartmouth 

                                    regimen)

                                    HUNCHAREK er al,Melanoma Res.11(2001):75-81(meta-analysis 

                                    from 20 randomized trials of  DTIC vs combination chemotherapy

                                    +/ -immunotherapy)

                                    LEGHA,Semin.Oncol.16(Suppl 1)(1989):34-44

                                    LUCE et al, Cancer Chemother. Rep. 54(1970):119-124 (5-day

                                    regimen)

                                    MIDDLETON et al,J.Clin.Oncol.18(2000):158-166(randomized                 

                                    phase III study of dacarbazine  vs temozolomide)                                                            PRITCHARD et al,Cancer Treat.Rep.64(1980):1123-1126(1-day

                                   regimen)

 

33.2.2                         Temozolomide

Temozolomide             200mg/m²                      p.o.                        d 1-5

To be repeated every 4 weeks

 

Literature:

MIDDLETON  et al, J.Clin.Oncol. 18(2000): 158-166(randomized phase III study of dacarbazine  vs temozolomide)

 

33.2.3                         Fotemustine

Fotemustine                 100mg/m²                  i.v.(1 h inf)                 d 1,8,15

To be repeated every 3 weeks

 

Literature:

            JACQUILLAT et al, Cancer 66 (1990):1873-1878

 

33.2.4                         Vindesine

Vindesine                        3mg/m²                    i.v.                              d 1

To be repeated every 2 weeks  for 1 year, then every 3 weeks for 6 months and finally every 4weeks for 6 months as adjuvant therapy.

 

 

Literature:

            RETSAS et al,Cancer 73 (1994):2129-2130

182                                                                                                                                     Malignant Melanoma

 

33.3                                Single agent therapy: biological therapy

 

33.3.1                         Interferon alpha

           Literature: for review e.g.

            AGARWALA  and KIRWOOD,Forum 10(2000):230-239

            EGGERMONT, Eur.J.Cancer 37(2001):2147-2153

            HANCOCK et al,Cancer Treat.Rev. 26(2000):81-89(adjuvant 

            therapy)

 

Only little activity of interferon  alpha has been demonstrated for metastatic stage IV melanoma. In the adjuvant setting for stage II and III disease a preliminary meta analysis has demonstrated a positive impact of interferon  alpha on relapse free but not on long-term overal survival. Before final results from a number of large randomized studies are available interferon alpha should not be considered as standard therapy.

                       

                        Low- dose interferon alpha

Interferon alpha           3MU                 s.c.3x weekly                6-36months

 

                        Literature:

                                    CASCINELLI et al,Lancet 358(2001) : 866-869(WHO Melanoma

                                    Program Trial 16)

                                    GROB et al, Lancet 351(1998):1905-1910(French trial)

                                    KIRKWOOD et al,J.Clin.Oncol.18(2000):2444-2458(first analysis

                                    of Intergroup trial E1690/S9111/C9190 comparing high-and low-

                                    dose interferon alpha).

                                    LAFUMA et al, Eur.J.Cancer 37(2001):369-375 (economic

                                    analysis of the French trial reported by Grob et al 1998)

                                    PEHAMBERGER et al,J.Clin.Oncol.16(1998):1425-1429(co-

                                    operative Austrian study ).

 

                        Intermediate-dose interferon alpha 

Interferon alpha         10MU         s.c.5 d/wk            for 4 wks followed by

                                   5MU           s.c.3x weekly       for 2 years

 

                        Literature:

                                    EGGERMONT et al, American Society of Clinical Oncology 2001

                                    Educational Book: 88-93 (preliminary results from EORTC 

                                    study18952)

 

                        High-dose interferon alpha

Interferon alpha        20MU/m²         i.v.(or i.m.) 5 d/wk         for 4 wks followed by

                                 10MU/m²           s.c. 3 x weekly              for 48 wks

         

           Literature:

            KIRKWOOD et al, J.Clin.Oncol.18(2000): 2444-2458 (first

            analysis  of Intergroup trial E 1690/S9111/C9190 comparing high-

            and low-dose interferon alpha)

 

33.3.2                         Interleukin –2

Literature: for review

            KEILHOLZ and EGGERMONT ,Cancer J.Sci.Am.6(Suppl 1)

            (2000):99-103(information from 27 trials of the EORTC programs

            on the use of interlookin 2 in stage IV melanoma patients)

            PHILIP and FLAHERTY,Semin.Oncol.24(Suppl 4)(1997):32-38

 

 

Malignant Melanoma                                                                                                                         183   

 

                       

Interleukin-2            600000 or 720000 IU/kg  i.v.(15min)every 8hours

                                 for  14 consecutive  doses over 5 days,as tolerated

                        After a six-to nine-day rest period,an additional 14 doses were scheduled

                        over the next  five days.Courses of therapy were usually separated by six-

                        to twelve-week intervals(max five).

 

                        Literature:

                                    ATKINS et al,J.Clin.Oncol.17(1999): 2105-2116(analysis of 270

                                    patients from eight clinical trials).

 

33.4                                Combination chemotherapy

 

33.4.1                         Dartmouth regimen(CBDT)

Cisplatin               25mg/m²            i.v.(30-45min inf)             d1-3

BCNU                 150mg/m²           i.v.(short inf)                     d1*

Dacarbazine        220mg/m²           i.v.(short inf)                     d1-3

Tamoxifen**      20-40mg              p.o.                         starting 1 wk before

                                                                                     chemotherapy and

                                                                                     continued as long as

                                                                                    patient is on treatment

To be repeated every 3 weeks

 *     BCNU repeated every odd 3-week cycle

 **   The addition of tamoxifen did  not provide a meaningful clinical  

        advantage

 

            Literature:

                        CHAPMAN et al,J.Clin.Oncol.17(1999):2745-2751 (randomized 

                        phase  III trial of  the  Dartmouth regimen vs dacarbazine

                        monotherapy)

                        CREAGAN et al,,J.Clin.Oncol.17(1999):1884-1890 (phase III trial

                        of cisplatin dacarbazine, and  BCNU with or without  tamoxifen)

                        MIDDLETON et al, Br.J.Cancer  82(2000):1158-1162

                        (randomized phase III study of  the Dartmouth regimen vs

                        dacarbazine + interferon alpha)

                        RUSTHOVEN et al,J.Clin.Oncol.14(1996):2083-2090(National 

                        Cancer Institute of Canada  Clinical Trials Group randomized,

                        double-blined , placebocontrolled  trial comparing   cisplatin,

                        dacarbazine ,and BCNU with or without tamoxifen)

 

33.4.2                         DVP

Dacarbazine                  250mg/m²              i.v.(30 min inf)              d1-5

Vindesine                      3mg/m²                  i.v.((bolus)                    d1,8,15

Cisplatin*                     100mg/m²               i.v.(30 min inf)              d1

To be repeated every 4 weeks (total of 3 cycles)

*    The addition  of cisplatin to dacarbazine/vindesine increased the 

      median time to progression, but not  overall survival. Toxicity was

       increased   as well.

 

Literature:

            JUNGNELIUS et al,Eur.J.Cancer 34(1998):1368-1374

 

33.5                                Biochemotherapy

The addition of immunotherapy to chemotherapy is still experimental and can not  be recommended for routine treatment in the absence of confirmatory randomized studies showing the benefit of that  approach.Only a few illustrating examples for  such protocol regimes are given.

 

 

184                                                                                                                        Malignant  Melanoma

                                      

33.5.1                         Dacarbazine + interferon alpha

Dacarbazine                800mg/m                   i.v.(short inf)           d 1

Interferon  alpha         9 MU                         s.c.                           3 x weekly

To be repeated every 3 weeks

 

Literature:

            MIDDLETON et al,J Cancer 82(2000):1158-1162 (randomized phase III study of the Dartmouth regimen vs   dacarbazine + interferon alpha)

 

33.5.2                         Dacarbazine + cisplatin +  interleukin-2 + interferon alpha

Dacarbazine               250mg/m²                i.v.(30 min inf)            d1-3 after

Cisplatin                    25mg/m²                   i.v.(1 h inf)                  d1-3

Interferon alpha         5MU/m²                   s.c.                         d6,8,10,13,15

Interleukin-2              18MU/m²                 i.v.(15 min inf)       d6-10,13-15

         To be repeated every 4 weeks (outpatient treatment possible)

 

Literature:

            FLAHERTY et al,J.Clin.Oncol.19(2001):3194 -3202